| |  Online-Ressource |
|---|
| Verfasst von: | Gerber, Angela [VerfasserIn]  |
|---|
| | Kirchhoff-Moradpour, Antje H. [VerfasserIn] |
|---|
| | Obieglo, Silke [VerfasserIn] |
|---|
| | Brandis, Matthias [VerfasserIn] |
|---|
| | Kirschfink, Michael [VerfasserIn] |
|---|
| | Zipfel, Peter F. [VerfasserIn] |
|---|
| | Goodship, Judith A. [VerfasserIn] |
|---|
| | Zimmerhackl, Lothar B. [VerfasserIn] |
|---|
| Titel: | Successful (?) therapy of hemolytic-uremic syndrome with factor H abnormality |
|---|
| Verf.angabe: | Angela Gerber, Antje H. Kirchhoff-Moradpour, Silke Obieglo, Matthias Brandis, Michael Kirschfink, Peter F. Zipfel, Judith A. Goodship, Lothar B. Zimmerhackl |
|---|
| E-Jahr: | 2003 |
|---|
| Jahr: | 26 June 2003 |
|---|
| Umfang: | 4 S. |
|---|
| Fussnoten: | Gesehen am 15.02.2021 |
|---|
| Titel Quelle: | Enthalten in: Pediatric nephrology |
|---|
| Ort Quelle: | Berlin : Springer, 1987 |
|---|
| Jahr Quelle: | 2003 |
|---|
| Band/Heft Quelle: | 18(2003), 9, Seite 952-955 |
|---|
| ISSN Quelle: | 1432-198X |
|---|
| Abstract: | We report a patient with continuously recurring hemolytic-uremic syndrome due to factor H deficiency. First at the age of 3 months he showed signs of hemolytic anemia, thrombocytopenia and renal insufficiency, often recurring concomitantly with respiratory tract infections, despite weekly to twice weekly plasma substitution (20 ml/kg body weight). Now at the age of 3.5 years glomerular filtration rate is approximately 50 ml/min/1.73 m(2) and psychomotoric development is normal. Since factor H is mainly synthesized in the liver, hepatic transplantation has been proposed as curative treatment. Before justification of liver transplantation as the ultimate treatment for these patients, an international registry should be developed to optimize and standardize therapeutic alternatives. |
|---|
| DOI: | doi:10.1007/s00467-003-1192-3 |
|---|
| URL: | Bitte beachten Sie: Dies ist ein Bibliographieeintrag. Ein Volltextzugriff für Mitglieder der Universität besteht hier nur, falls für die entsprechende Zeitschrift/den entsprechenden Sammelband ein Abonnement besteht oder es sich um einen OpenAccess-Titel handelt.
Volltext: https://doi.org/10.1007/s00467-003-1192-3 |
|---|
| | DOI: https://doi.org/10.1007/s00467-003-1192-3 |
|---|
| Datenträger: | Online-Ressource |
|---|
| Sprache: | eng |
|---|
| Sach-SW: | Child, Preschool |
|---|
| | Complement Factor H |
|---|
| | Hemolytic-Uremic Syndrome |
|---|
| | Humans |
|---|
| | Infant |
|---|
| | Kidney Failure, Chronic |
|---|
| | Male |
|---|
| | Plasma Substitutes |
|---|
| | Plasmapheresis |
|---|
| K10plus-PPN: | 1748325981 |
|---|
| Verknüpfungen: | → Zeitschrift |
|---|
Successful (?) therapy of hemolytic-uremic syndrome with factor H abnormality / Gerber, Angela [VerfasserIn]; 26 June 2003 (Online-Ressource)
